The objective of this document is to guide diagnosis and management of patients with rare coagulation disorders in the UK. The disorders described in this document include heritable deficiencies of fibrinogen, prothrombin, factor (F) V, FVII, FX, FXI and FXIII, combined FV and FVIII deficiency and vitamin K-dependent coagulation factor deficiency.

Declaration of Interests

The BSH paid the expenses incurred during the writing of this guidance. None of the authors had conflicts of interest to declare. All authors have made a declaration of interests to the BSH and Task Force Chairs which may be viewed on request.